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Video: Koj puas tuaj yeem muaj Marfan syndrome thiab tsis siab?
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2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Tsis yog txhua tus neeg siab los yog nyias lossis qhov muag pom muaj tus kab mob. Cov neeg uas muaj Marfan syndrome Cov tsos mob tshwj xeeb uas feem ntau tshwm sim ua ke, thiab nws yog tus qauv no uas cov kws kho mob nrhiav thaum kuaj pom nws.
Tom qab ntawd, ib tus tuaj yeem nug, koj puas tuaj yeem muaj mob Marfan syndrome?
Thaum feem ntau ntawm Marfan syndrome: cov tsos mob tau txais qub txeeg qub teg, qee qhov yog vim muaj kev hloov pauv ntawm tus kheej, tsis muaj keeb kwm tsev neeg. Marfan syndrome tuaj yeem ua tau ua mob me mus rau qhov hnyav, thiab tuaj yeem ua rau hnyav nrog lub hnub nyoog, nyob ntawm thaj chaw twg cuam tshuam thiab mus rau qib twg. Hauv Marfan syndrome: cov tsos mob , lub plawv feem ntau cuam tshuam.
Kuj Paub, vim li cas cov neeg uas muaj Marfan syndrome siab? Marfan syndrome: cov tsos mob yog tshwm sim los ntawm qhov tsis xws luag hauv cov noob hu ua fibrillin-1. Fibrillin-1 ua lub luag haujlwm tseem ceeb ua lub tsev thaiv rau cov nqaij sib txuas hauv lub cev. Cov noob tsis xws luag kuj ua rau cov pob txha ntev ntawm lub cev loj tuaj. Cov neeg nrog qhov no tus mob muaj siab siab thiab ntev caj npab thiab txhais ceg.
Ntawm no, tus neeg nruab nrab siab npaum li cas nrog Marfan syndrome?
Cov txhais tau tias MFS cov neeg laus qhov siab yog 189.8 ± 4.4 cm, thiab nws yog siab tshaj 97 feem pua rau Korean cov neeg laus txiv neej (184.2 ± 5.9 cm, P<0.001). Kev loj hlob nkhaus ntawm cov neeg mob nrog Marfan syndrome: cov tsos mob . (A) Txiv neej.
Vim li cas tib neeg nrog Marfan yuag yuag?
Teb • Marfan cov Syndrome yog ib yam kab mob tsis tshua muaj ntawm collagen - ib qho protein uas muab feem ntau ntawm cov qauv rau cov nqaij mos hauv peb lub cev. Cov neeg nrog Marfan's syndrome yuav tsum siab thiab nyias , nrog cov caj npab ntev thiab cov ntiv tes tsis sib xws.
Pom zoo:
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Thaum niam txiv muaj tus mob Marfan, txhua tus ntawm nws tus menyuam muaj 50 feem pua muaj feem (1 lub sijhawm hauv 2) kom tau txais FBN1 noob. Thaum Marfan syndrome tsis yog ib txwm tau txais, nws ib txwm muaj txiaj ntsig
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Thaum lub tshuab ua pa tawm, lub siab toj siab (Pplat) yog lub zog siv thaum kawg ntawm kev tshoov siab rau cov cua me thiab txoj kev alveoli thiab nws tau ntsuas thaum lub sijhawm ua rau lub zog nqus (lossis tuav) ntawm lub tshuab ua pa. Ob qhov kev tsav tsheb siab (DP) thiab kev ua raws kev ua pa (Cpl, rs) suav nrog Pplat
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Qhov ua rau yog collagenous colitis, uas ua rau raws plab, nqhis dej heev thiab tsis tuaj yeem nqus tau cov as -ham. Qaug zog, ntshai, hnov mob plab, pw tsis tsaug zog, tsis muaj zog, ntshav siab, palpitations, tsis meej pem, thiab kiv taub hau yog kuv cov tsos mob ntawm cov poov tshuaj tsawg
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Kev saib xyuas mob hlwb yog ib ceg tshwj xeeb ntawm kev saib xyuas neeg mob nrog kev tsom mus rau kev saib xyuas cov neeg muaj kev puas siab puas ntsws lossis kev nyuaj siab. Cov kws saib xyuas mob hlwb ua haujlwm nrog cov neeg mob uas raug kev txom nyem los ntawm kev ntxhov siab, kev nyuaj siab, schizophrenia, kev puas siab puas ntsws bipolar thiab ntau lwm tus