Cov txheej txheem:
![Qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome yog dab tsi? Qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome yog dab tsi?](https://i.answers-medical.com/preview/medical-health/14070476-what-is-the-difference-between-myasthenia-gravis-and-lambert-eaton-syndrome-j.webp)
Video: Qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome yog dab tsi?
![Video: Qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome yog dab tsi? Video: Qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome yog dab tsi?](https://i.ytimg.com/vi/pP-EopWAP-M/hqdefault.jpg)
2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Cov qhov sib txawv ntawm LEMS thiab myasthenia gravis (MG)
Qhov no zoo ib yam li myasthenia gravis , txawm li cas los xij lub hom phiaj ntawm kev tawm tsam yog txawv hauv MG raws li acetylcholine receptor ntawm lub paj hlwb tau cuam tshuam, hos hauv LEMS nws yog qhov hluav taws xob-gated calcium channel ntawm cov hlab ntsha.
Tom qab ntawd, cov tsos mob ntawm Lambert Eaton yog dab tsi?
Nov yog cov tsos mob ntawm Lambert-Eaton syndrome:
- Cov leeg tsis muaj zog - tsis muaj zog feem ntau tso tseg ib ntus tom qab ua haujlwm lossis ua haujlwm hnyav.
- Teeb meem taug kev.
- Tingling hnov ntawm txhais tes lossis ko taw.
- Daim tawv muag poob.
- Qaug zog.
- Qhov ncauj qhuav.
- Teeb meem hais lus thiab nqos.
- Teeb meem ua tsis taus pa.
Kuj Paub, dab tsi zoo ib yam li myasthenia gravis? Ceev faj: muaj lwm yam kab mob uas ua rau mob myasthenia . Tus lej ntawm cov teeb meem tuaj yeem ua raws MG, suav nrog kev qaug zog, amyotrophic lateral sclerosis (ALS), Lambert-Eaton myasthenic syndrome, botulism, ua rau penicillamine myasthenia , thiab congenital myasthenic syndromes.
Yog li ntawd, Eaton Lambert Syndrome yog dab tsi?
Lambert - Eaton myasthenic tus mob (LEMS) yog kab mob autoimmune - kab mob uas lub cev tiv thaiv kab mob ua rau lub cev muaj cov nqaij mos. Qhov kev tawm tsam tshwm sim ntawm kev sib txuas ntawm cov hlab ntsha thiab cov leeg (cov leeg sib txuas neuromuscular) thiab cuam tshuam nrog kev muaj peev xwm ntawm cov leeg hlwb kom xa cov cim rau cov leeg nqaij.
Dab tsi ua rau Lambert Eaton syndrome?
Lambert – Eaton myasthenic tus mob yog ua los ntawm autoantibodies mus rau daim nyias nyias presynaptic. Myasthenia gravis yog ua los ntawm autoantibodies mus rau postsynaptic acetylcholine receptors. Lambert – Eaton myasthenic tus mob (LEMS) yog ib qho autoimmune uas tsis tshua muaj tsis meej pem yam ntxwv ntawm cov leeg nqaij tsis muaj zog.
Pom zoo:
Dab tsi yog qhov sib txawv ntawm qhov kev cia siab rau qhov ntim thiab qhov ntim cia tseg?
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Qhov ntim cia tseg (ERV) yog cov pa ntxiv uas tuaj yeem nqus tau tom qab ua pa ib txwm. Nws yog qhov nyiaj khaws cia uas tuaj yeem nqus tau dhau qhov uas ib txwm muaj. Hloov pauv, qhov ua rau lub zog cia siab (IRV) yog qhov ntxiv ntawm huab cua uas tuaj yeem nqus tau tom qab nqus tau ib txwm
Dab tsi yog qhov sib txawv thiab qhov zoo sib xws ntawm cov khoom sib tsoo thiab qhov kov zoo?
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Dab tsi yog qhov sib txawv thiab qhov zoo sib xws ntawm 'crude' kov thiab 'nplua' kov qhov hnov? Nyuaj kov yog hais txog kev nkag siab los ntawm kev txhawb nqa ntawm cov neeg txais khoom ntawm qhov tsis nkag siab nrog cov teb loj. Hauv kev sib piv, kev kov zoo yog hais txog cov neeg txais khoom ntawm kev nkag siab siab nrog cov chaw txais me me
Dab tsi yog qhov txawv ntawm ER ntxhib thiab du ER Dab tsi yog ER ua qhov sib txawv hauv txhua kis?
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Ob qho tib si du thiab ntxhib endoplasmic reticulum pab hauv kev tsim thiab khaws cov proteins Qhov sib txawv tseem ceeb yog tias ib qho muaj ribosomes rau nws thiab lwm yam tsis. Rough ER zoo li cov nplooj ntawv. RER sib sau ua (ua) thiab ntim cov protein. RER tau txuas nrog lub nuclear membrane
Dab tsi yog qhov txawv ntawm cheeb tsam sib txawv thiab thaj tsam tas li ntawm ib qho tshuaj tiv thaiv?
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Cov cheeb tsam sib txawv no, muaj li ntawm 110-130 amino acids, muab cov tshuaj tiv thaiv kab mob nws qhov tshwj xeeb rau kev khi antigen. Cov cheeb tsam sib txawv suav nrog qhov kawg ntawm lub teeb thiab cov saw hnyav. Lub cheeb tsam tas li txiav txim siab cov txheej txheem siv los rhuav tshem antigen
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Qhov pib tsis txaus yog qhov tsawg kawg ntawm kev txhawb siab xav tau rau ib tus neeg kom pom qhov kev txhawb siab 50 feem pua ntawm lub sijhawm. Qhov sib txawv ntawm qhov sib txawv yog qhov sib txawv me tshaj hauv kev txhawb nqa uas tuaj yeem kuaj pom 50 feem pua ntawm lub sijhawm