Cov txheej txheem:

Qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome yog dab tsi?
Qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome yog dab tsi?

Video: Qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome yog dab tsi?

Video: Qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome yog dab tsi?
Video: Lambert -Eaton Myasthenic Syndrome 2024, Lub rau hli ntuj
Anonim

Cov qhov sib txawv ntawm LEMS thiab myasthenia gravis (MG)

Qhov no zoo ib yam li myasthenia gravis , txawm li cas los xij lub hom phiaj ntawm kev tawm tsam yog txawv hauv MG raws li acetylcholine receptor ntawm lub paj hlwb tau cuam tshuam, hos hauv LEMS nws yog qhov hluav taws xob-gated calcium channel ntawm cov hlab ntsha.

Tom qab ntawd, cov tsos mob ntawm Lambert Eaton yog dab tsi?

Nov yog cov tsos mob ntawm Lambert-Eaton syndrome:

  • Cov leeg tsis muaj zog - tsis muaj zog feem ntau tso tseg ib ntus tom qab ua haujlwm lossis ua haujlwm hnyav.
  • Teeb meem taug kev.
  • Tingling hnov ntawm txhais tes lossis ko taw.
  • Daim tawv muag poob.
  • Qaug zog.
  • Qhov ncauj qhuav.
  • Teeb meem hais lus thiab nqos.
  • Teeb meem ua tsis taus pa.

Kuj Paub, dab tsi zoo ib yam li myasthenia gravis? Ceev faj: muaj lwm yam kab mob uas ua rau mob myasthenia . Tus lej ntawm cov teeb meem tuaj yeem ua raws MG, suav nrog kev qaug zog, amyotrophic lateral sclerosis (ALS), Lambert-Eaton myasthenic syndrome, botulism, ua rau penicillamine myasthenia , thiab congenital myasthenic syndromes.

Yog li ntawd, Eaton Lambert Syndrome yog dab tsi?

Lambert - Eaton myasthenic tus mob (LEMS) yog kab mob autoimmune - kab mob uas lub cev tiv thaiv kab mob ua rau lub cev muaj cov nqaij mos. Qhov kev tawm tsam tshwm sim ntawm kev sib txuas ntawm cov hlab ntsha thiab cov leeg (cov leeg sib txuas neuromuscular) thiab cuam tshuam nrog kev muaj peev xwm ntawm cov leeg hlwb kom xa cov cim rau cov leeg nqaij.

Dab tsi ua rau Lambert Eaton syndrome?

Lambert – Eaton myasthenic tus mob yog ua los ntawm autoantibodies mus rau daim nyias nyias presynaptic. Myasthenia gravis yog ua los ntawm autoantibodies mus rau postsynaptic acetylcholine receptors. Lambert – Eaton myasthenic tus mob (LEMS) yog ib qho autoimmune uas tsis tshua muaj tsis meej pem yam ntxwv ntawm cov leeg nqaij tsis muaj zog.

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