Grey platelet syndrome yog dab tsi?
Grey platelet syndrome yog dab tsi?

Video: Grey platelet syndrome yog dab tsi?

Video: Grey platelet syndrome yog dab tsi?
Video: Grey Platelet Syndrome .... Explained 2024, Lub Xya hli ntuj
Anonim

Grey platelet syndrome (GPS), los yog platelet alpha-granule deficiency, yog qhov tsis tshua muaj menyuam los ntawm lub cev autosomal los ntshav tsis meej pem tshwm sim los ntawm kev txo lossis tsis muaj alpha-granules hauv ntshav cov platelets , thiab tso tawm cov protein ib txwm muaj nyob rau hauv cov granules rau hauv cov pob txha, ua rau myelofibrosis.

Tsis tas li ntawd, Scott syndrome yog dab tsi?

Scott tus syndrome yog ib qho tsis tshua muaj ntshav los tsis xwm yeem uas yog los ntawm qhov tsis xws luag hauv cov txheej txheem platelet xav tau rau ntshav coagulation. Hauv Scott Syndrome , cov txheej txheem rau translocating PS mus rau platelet membrane yog qhov tsis zoo, ua rau muaj kev cuam tshuam ntawm thrombin.

Tsis tas li, cov tsos mob ntawm GPS yog dab tsi? Cov tsos mob thiab cov tsos mob feem ntau tshwm sim thaum yug los lossis thaum yau thiab muaj xws li tsawg platelet suav , yooj yim nqaij tawv, ntshav ntev, thiab qhov ntswg los ntshav. Cov neeg mob feem ntau muaj myelofibrosis thiab splenomegaly.

Kuj paub, dab tsi yog Hypogranular platelets?

Cov dawb platelet Syndrome (WPS) yog ib qho autosomal dominantly inherited hypogranular platelet cov Cov teeb meem tshwm sim los ntawm qhov muaj cov Golgi complexes los ntawm niam txiv megakaryocytes hauv 13% lossis ntau dua ntawm lawv cov kev ncig. cov platelets.

Cov platelets loj heev txhais li cas?

" Cov platelet loj heev "yog lo lus siv los piav qhia cov platelets uas txawv txav loj , i.e.,ua loj raws li cov qe ntshav liab ib txwm muaj. Cov no tuaj yeem pom nyob rau hauv qee yam mob xws li kev tiv thaiv kab mob thrombocytopenic purpura (ITP) lossis hauv cov kab mob tsis tshua muaj xws li Bernard-Soulier kab mob.

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