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Video: Puas yog Russell Silver syndrome puas xiam oob qhab?
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2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Russell - Nyiaj Syndrome thiab kev kawm tsis siv lus xiam oob qhab : ib rooj plaub kawm. Russell - Nyiaj Syndrome (RSS) yog qhov tsis tshua muaj kev loj hlob ntawm caj ces tsis meej pem yam ntxwv ntawm kev loj hlob ntawm cev xeeb tub thiab tom qab yug me nyuam qeeb thiab lwm yam kev txawv txav ntawm lub cev.
Ua qhov no hauv kev txiav txim siab, puas yog Russell Silver syndrome yog daim ntawv ntawm kev ntsiag to?
Nyiaj โ Russell syndrome ua rau (SRS), kuj hu ua Nyiaj โ Russell dwarfism los yog Russell โ Nyiaj Syndrome (RSS) yog kev loj hlob tsis meej pem tshwm sim hauv kwv yees li 1/50, 000 txog 1/100, 000 yug. Nws yog ib ntawm 200 hom ntawm dwarfism thiab ib ntawm tsib hom ntawm primordial dwarfism.
Ib sab saum toj no, cov tsos mob ntawm Russell Silver syndrome yog dab tsi? Cov tsos mob
- Kev txwv kev loj hlob hauv plab (tsis loj hlob ua ntej yug)
- Tsawg yug me nyuam hnyav.
- Lub taub hau uas pom loj hauv kev sib piv rau lub cev loj (txheeb ze macrocephaly)
- Tsis qab los noj mov thiab noj teeb meem.
- Hypoglycemia.
- Kev loj hlob tsis zoo tom qab yug los, ua rau lub cev luv.
- Scoliosis.
- Nkhaus ntawm tus ntiv tes pinky (clinodactyly)
Ib yam li ntawd, koj yuav nug, Puas yog Russell Silver syndrome kho tau?
Kev kho mob rau Russell - Nyiaj Syndrome Kev kho mob kom pab nrog kev loj hlob thiab kev txhim kho suav nrog: cov sijhawm noj zaub mov zoo nrog cov khoom noj txom ncauj tshwj xeeb thiab sijhawm noj mov. kev loj hlob hormone txhaj. luteinizing hormone-tso kev kho (cov tshuaj tso tawm hauv poj niam kom ua rau muaj qe menyuam txhua hli)
Lub neej kev cia siab ntawm ib tus neeg nrog Russell Silver syndrome yog dab tsi?
Txawm hais tias cov tub ntxhais hluas thiab cov neeg laus nrog Russell - Nyiaj Syndrome yuav luv dua qhov nruab nrab, tus tus mob tsis cuam tshuam loj lub neej cia siab . Russell - Nyiaj Syndrome tam sim no xav tias yog teeb meem caj ces, tshwm sim los ntawm kev txawv txav hauv chromosome 7 lossis chromosome 11.
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