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Alpha thiab beta thalassemia yog dab tsi?
Alpha thiab beta thalassemia yog dab tsi?

Video: Alpha thiab beta thalassemia yog dab tsi?

Video: Alpha thiab beta thalassemia yog dab tsi?
Video: Beta Thalassemia - causes, symptoms, diagnosis, treatment, pathology 2024, Lub rau hli ntuj
Anonim

Cov thalassemias yog ib pab pawg ntawm cov kab mob hematologic uas tau tshwm sim los ntawm kev ua tsis zoo hauv kev sib xyaw ntawm ib lossis ntau ntawm cov hemoglobin saw. Alpha thalassemia yog tshwm sim los ntawm kev txo lossis tsis tuaj ua ke ntawm alpha globin chains, thiab beta thalassemia yog tshwm sim los ntawm kev txo lossis tsis tuaj ua ke ntawm beta globin cov saw.

Yooj yim li ntawd, ib tus neeg puas tuaj yeem muaj ob qho alpha thiab beta thalassemia?

Yog - alpha thiab beta thalassemia - Hgb A2 yog qhov taw qhia siab beta thalassemia . Ntau qhov microcytosis ntau dua li qhov xav tau thiab hloov pauv noob (yog li alpha thalassemia ). Hgb li qub vim tias nws yog kev hloov pauv sib npaug.

Kuj Paub, 4 hom alpha thalassemia yog dab tsi? Muaj plaub hom alpha thalassemia , hemoglobin Bart hydrops fetalis syndrome lossis Hb Bart syndrome (daim ntawv hnyav dua), Kab mob HbH, lub xeev tus neeg nqa khoom ntsiag to thiab tus yam ntxwv. Alpha thalassemia tshwm sim ntau zaus hauv tib neeg los ntawm Mediterranean lub tebchaws, North Africa, Middle East, India, thiab Central Asia.

Hauv qhov no, Thalassemia Alpha yog dab tsi?

Alpha thalassemia yog ntshav tsis meej uas txo qis kev tsim cov hemoglobin. Hemoglobin yog cov protein hauv cov qe ntshav liab uas nqa cov pa oxygen mus rau cov cell thoob plaws lub cev. Hom mob hnyav tshaj plaws hu ua hemoglobin Bart hydrops fetalis syndrome, uas tseem hu ua Hb Bart syndrome lossis alpha thalassemia loj.

Cov tsos mob ntawm alpha thalassemia yog dab tsi?

Qee qhov tshwm sim ntau ntawm alpha thalassemia suav nrog:

  • qaug zog, qaug zog, lossis ua tsis taus pa.
  • tsos nqaij daim tawv lossis daj daj rau ntawm daim tawv nqaij (jaundice)
  • chim siab.
  • deformities ntawm lub ntsej muag pob txha.
  • kev loj hlob qeeb
  • lub plab o.
  • zis zis.

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