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2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
"Microangiopathic hemolytic ntshav tsis txaus MAHA ) "tam sim no tau siv los txheeb xyuas ib qho hemolytic anemia ntsig txog RBC kev faib ua feem, tshwm sim hauv kev koom tes nrog kab mob hlab ntsha me. DIC , RBC fragmentation yog xav los ntawm kev tso cov fibrin lossis platelets hauv microvasculature.
Ntxiv mus, dab tsi ua rau Maha?
Txhua yam ua , mechanism ntawm MAHA yog kev tsim cov fibrin mesh vim nce kev ua haujlwm ntawm cov txheej txheem ntawm coagulation. Cov qe ntshav liab raug txiav lub cev los ntawm cov protein sib txuas. Cov khoom tawg ua ke yog schistocytes pom hauv lub teeb tsom me me.
Kuj Paub, dab tsi ua rau Microangiopathic hemolytic anemia? Microangiopathic hemolytic anemia Muaj ntau ntau ua , suav nrog kev kis mob (ua rau, piv txwv li hauv kev nthuav tawm cov hlab ntshav coagulation (Daim duab 26.8) lossis los ntshav uraemic syndrome), kev raug mob ntawm lub cev (piv txwv li los ntawm lub plawv ua haujlwm li qub) thiab autoimmune (piv txwv li thrombotic thrombocytopenic purpura).
Ib sab saum toj no, TTP puas tuaj yeem ua rau DIC?
TTP -HUS and DIC tuaj yeem ua tau feem ntau yog qhov txawv ntawm qhov tshwm sim ntawm lawv tshwm sim hauv cov chaw kho mob sib txawv (piv txwv li, raug mob lossis sepsis rau DIC thiab kub cev cuam tshuam nrog thrombocytopenia thiab microangiopathic hemolytic anemia rau TTP -HUS). Thrombocytopenia muaj nyob hauv ob qho tib si DIC thiab tiv thaiv kab mob thrombocytopenic purpura (ITP).
Microangiopathic hemolytic anemia kho tau li cas?
Kev kho thawj kab: Kev sib pauv ntshav sai yog thawj txoj kab kev kho mob rau TTP-HUS. Kev sib pauv ntshav tuaj yeem rov ua tiav qib ADAMTS13 (yog tias tus neeg mob tsis txaus), tshem tawm qhov tsis txawv txav loj von Willebrand qhov ntau yam sib txawv uas tab tom pib microangiopathic tshuaj txheej txheem thiab tshem tawm autoantibodies qhia tawm tsam ADAMTS13.
Pom zoo:
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Differential Diagnosis: Kev nyuaj siab loj heev
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