![Dab tsi yog qhov ua rau tsis muaj enzyme? Dab tsi yog qhov ua rau tsis muaj enzyme?](https://i.answers-medical.com/preview/medical-health/13911145-what-is-the-cause-of-enzyme-deficiency-j.webp)
Video: Dab tsi yog qhov ua rau tsis muaj enzyme?
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2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Tsis txaus enzyme , los yog tsis muaj cov no cov enzymes , tau txais qhov tsis xws luag tshwm sim hauv ntau qhov kev hloov pauv lub neej lossis teeb meem kev phom sij rau lub neej: MPS: Cov mucopolysaccharidoses yog ib pab pawg ntawm cov kab mob qub txeeg qub teg uas muaj qhov tsis zoo lossis ploj mus enzyme ua cov piam thaj sib xyaw ua ke kom sib sau hauv cov cell.
Kuj paub, puas muaj cov enzyme tsis txaus?
Kev tsis muaj enzyme anemias Ob feem ntau tsis xws luag yog cov piam thaj-6-phosphate dehydrogenase (G6PD) tsis txaus thiab pyruvate kinase (PK) tsis txaus.
Ib yam nkaus, koj yuav paub tau li cas yog tias koj muaj qhov tsis txaus enzyme?
- Raws plab. EPI tuaj yeem ua teeb meem nrog zaub mov tsis tau txav nrawm dhau los ntawm txoj hnyuv.
- Roj thiab tsam plab.
- Mob plab.
- Foul-tsw, quav quav (steatorrhea)
- Poob phaus.
Tsis tas li kom paub yog, yuav kho tus tsis txaus enzyme li cas?
Koj tus kws kho mob yuav pib koj daim ntawv xaj tshuaj kev kho mob npe hu ua pancreatic enzyme hloov kho, lossis PERT. PERTs yog lub ntsiab kev kho mob rau EPI-lawv hloov cov zom zaub mov cov enzymes tias koj lub txiav tsis tsim tawm lawm. Thaum noj nrog zaub mov, PERTs pab zom cov khoom noj hauv cov zaub mov.
Yuav ua li cas yog tias ib qho enzyme ploj lossis puas?
Phenylketonuria (PKU) yog qhov xwm txheej tsis tshua muaj caj ces uas ua rau muaj cov amino acid hu ua phenylalanine los txhim kho hauv lub cev. Thaum twg qhov no enzyme ploj lawm , koj lub cev tsis tuaj yeem zom phenylalanine. Qhov no ua rau muaj kev sib sau ntawm phenylalanine hauv koj lub cev. Cov menyuam mos hauv Tebchaws Meskas tau tshuaj xyuas PKU sai tom qab yug los.
Pom zoo:
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