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Video: Yuav kuaj li cas thiaj li tsis muaj lipase?
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2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Kev kuaj mob . Cov kev kuaj mob ntawm tsev neeg lipoprotein tsis muaj lipase Thaum kawg tau lees paub los ntawm kev kuaj pom ntawm homozygous lossis sib xyaw heterozygous pathogen gene variants hauv LPL nrog qis lossis qis lipoprotein lipase cov kev ua haujlwm ntawm enzyme.
Ib yam nkaus, yuav kho li cas lipoprotein lipase deficiency?
Ib feem ntawm LPL cov neeg tsis muaj peev xwm tuaj yeem ua tiav kho los ntawm kev txwv kev noj zaub mov ntawm cov rog, tab sis ntau tus tseem tab tom muaj teeb meem los ntawm kev mob plab rov qab thiab ntu mob pancreatitis. Lub hom phiaj ntawm kev txwv cov rog kom tsawg yog txo chylomicronemia thiab hypertriglyceridemia txaus los tiv thaiv cov tsos mob.
Tom qab ntawd, lo lus nug yog, Hyperchylomicronemia yog dab tsi? Hyperchylomicronemia . 11766. Tsev neeg Hyperchylomicronemia , kuj tseem hu ua Type I Dyslipidemia, yog kab mob uas tsis tshua pom muaj tus yam ntxwv los ntawm kev tsim cov chylomicrons, lipoproteins nqa roj thiab roj cholesterol hauv cov ntshav.
Qhov thib ob, dab tsi ua rau lub siab lipase ua?
Ib qho ntawm cov haujlwm tseem ceeb ntawm lub siab lipase yog los hloov cov lipoprotein nruab nrab-ntom (IDL) mus rau qhov qis-ntom lipoprotein (LDL). Hepatic lipase yog li ua lub luag haujlwm tseem ceeb hauv kev tswj cov qib triglyceride hauv cov ntshav los ntawm kev tswj hwm qib qis ntawm IDL, HDL thiab LDL.
Tsev neeg Chylomicronemia syndrome yog dab tsi?
Tsev neeg chylomicronemia syndrome (FCS) yog qhov loj kab mob uas tiv thaiv lub cev los ntawm kev tawg cov rog. Kev noj zaub mov txawm tias muaj roj me me tuaj yeem ua rau ib tus neeg muaj mob FCS, thiab tus mob ua rau muaj cov tsos mob ntev thiab tuaj yeem ua rau muaj mob ua rau tuag taus. FCS yog caj ces tsis meej pem dhau los ntawm niam txiv.
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