Multiple Endocrine Neoplasia syndrome hom 2 yog dab tsi?
Multiple Endocrine Neoplasia syndrome hom 2 yog dab tsi?

Video: Multiple Endocrine Neoplasia syndrome hom 2 yog dab tsi?

Video: Multiple Endocrine Neoplasia syndrome hom 2 yog dab tsi?
Video: Multiple Endocrine Neoplasia 2 2024, Lub Xya hli ntuj
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Ntau yam endocrine neoplasia hom 2 (tseem hu ua "Pheochromocytoma thiab amyloid ua cov qog nqaij hlav qog nqaij hlav hauv siab", "PTC tus mob , "thiab" Sipple tus mob ") yog pab pawg ntawm kev kho mob cuam tshuam nrog cov qog nqaij hlav ntawm cov endocrine lawv. Cov qog nqaij hlav tuaj yeem ua rau benign lossis malignant (mob qog noj ntshav).

Hais txog qhov no, ntau yam kab mob endocrine neoplasia hom 2 yog dab tsi?

Ntau yam endocrine neoplasia hom 2 (MEN2) yog ib qho xwm txheej uas cuam tshuam nrog 3 thawj hom ntawm cov qog nqaij hlav: qog nqaij hlav qog noj ntshav hauv nruab nrab, cov qog parathyroid, thiab pheochromocytoma. MEN2 tau muab cais ua subtypes raws li cov yam ntxwv kho mob.

Tom qab ntawd, lo lus nug yog, ntau yam kab mob endocrine neoplasia yog dab tsi? Ntau yam endocrine neoplasia syndromes tsis tshua muaj tshwm sim, muaj teeb meem tshwm sim hauv ntau yam cov endocrine qog tsim cov qog nqaij hlav tsis zoo (benign) lossis mob qog noj ntshav (mob qog noj ntshav) lossis loj hlob ntau dhau yam tsis tsim cov qog. Ntau yam endocrine neoplasia syndromes yog tshwm sim los ntawm kev hloov noob, yog li lawv zoo li khiav hauv tsev neeg.

Ua qhov no saib, dab tsi yog cov tsos mob ntawm ntau yam endocrine neoplasia?

Cov tsos mob. Cov tsos mob ntawm ntau yam kab mob endocrine neoplasia hom 1, lossis MEN 1, suav nrog kev nkees, mob pob txha, pob txha tawg, pob zeb hauv lub raum, thiab mob txhab hauv plab lossis hnyuv. Cov tsos mob tshwm sim los ntawm kev tso tawm ntau cov tshuaj hormones hauv lub cev.

Ntau npaum li cas yog ntau yam endocrine neoplasia?

Ntau yam endocrine neoplasia hom 1 cuam tshuam txog 1 hauv 30, 000 tus neeg; ntau yam endocrine neoplasia hom 2 cuam tshuam rau kwv yees li 1 ntawm 35,000 tus neeg. Ntawm cov subtypes ntawm hom 2, hom 2A yog qhov ntau tshaj ntau daim ntawv, ua raws los ntawm FMTC. Hom 2B tsis tshua muaj neeg pom, suav txog li 5 feem pua ntawm txhua kis ntawm hom 2.

Pom zoo: