Sideroblastic anemia kuaj tau li cas?
Sideroblastic anemia kuaj tau li cas?

Video: Sideroblastic anemia kuaj tau li cas?

Video: Sideroblastic anemia kuaj tau li cas?
Video: Sideroblastic Anemia ( Clear & Complete Explain ) 2024, Lub Xya hli ntuj
Anonim

Kev kuaj mob . Sideroblastic anemia xav tias yog cov neeg mob microcytic ntshav ntshav lossis RDW siab ntshav ntshav , tshwj xeeb tshaj yog nrog nce ntshav hlau, ntshav ferritin, thiab transferrin saturation (saib Iron Deficiency Ntshav Qab Zib ). Cov tshuaj pleev ib ce qhia pom RBC dimorphism.

Yog li ntawd, koj yuav tshuaj xyuas Sideroblastic anemia li cas?

Diagnostic workup rau sideroblastic anemia tej zaum yuav suav nrog kev ua haujlwm ntshav (suav cov ntshav tag nrho, cov hlab ntsha ib ncig, kev tshawb fawb hlau) thiab pob txha pob txha txoj kev xav thiab/lossis kuaj ntshav.

Tsis tas li ntawd, hom ntshav qab zib hom twg yog Sideroblastic? Sideroblastic anemia , los yog sideroachrestic ntshav ntshav , yog a daim ntawv ntawm anemia nyob rau hauv uas cov pob txha tsim tawm ringed sideroblasts es tsis noj qab nyob zoo cov qe ntshav liab (erythrocytes).

Tsis tas li ntawd, cov tsos mob ntawm Sideroblastic anemia yog dab tsi?

Cov cim & Cov tsos mob Cov sideroblastic anemias yog tus cwj pwm los ntawm qaug zog, ua tsis taus pa nyuaj, thiab kev xav tsis muaj zog. Hauv kev tawm dag zog, cov neeg uas muaj qhov teeb meem no yuav hnov mob zoo li angina. Ntau hom ntawv ntawm ntshav ntshav yog tshwm sim los ntawm cov hlau tsis txaus hauv cov ntshav.

Vim li cas ntshav ntshav siab hauv Sideroblastic anemia?

Vim hlau Tsis siv neeg hloov pauv saturation yog nce (> 80%) thiab ntshav qab zib LDH yog nce (tsis muaj txiaj ntsig erythropoiesis). Tau txais sideroblastic anemia feem ntau yog cov pov thawj ntxov tshaj plaws ntawm myelodysplastic syndrome (MDS) - cov khoom siv hluav taws xob ntshav ntshav nrog ringed sideroblasts . Hauv lub sijhawm hlau tshaj yuav ua teeb meem.

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