Puas yog Russell Silver syndrome yog daim ntawv ntawm kev ntsiag to?
Puas yog Russell Silver syndrome yog daim ntawv ntawm kev ntsiag to?

Video: Puas yog Russell Silver syndrome yog daim ntawv ntawm kev ntsiag to?

Video: Puas yog Russell Silver syndrome yog daim ntawv ntawm kev ntsiag to?
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Nyiaj โ€“ Russell syndrome ua rau (SRS), kuj hu ua Nyiaj โ€“ Russell dwarfism los yog Russell โ€“ Silver Syndrome (RSS) yog kev loj hlob tsis meej pem tshwm sim hauv kwv yees li 1/50, 000 txog 1/100, 000 yug. Nws yog ib ntawm 200 hom dwarfism thiab ib ntawm tsib hom ntawm primordial dwarfism.

Ntxiv mus, puas yog Russell Silver syndrome ua tsis taus?

Russell - Silver Syndrome thiab kev kawm tsis hais lus kev tsis taus : ib rooj plaub kawm. Russell - Nyiaj Syndrome (RSS) yog qhov tsis tshua muaj kev loj hlob ntawm caj ces yam ntxwv ntawm kev loj hlob ntawm cev xeeb tub thiab tom qab yug me nyuam qeeb thiab lwm yam kev txawv txav ntawm lub cev.

Ib qho ntxiv, puas yog Russell Silver syndrome caj ces? Feem ntau ntawm Russell - Silver Syndrome tsis tu ncua, uas txhais tau tias lawv tshwm sim hauv tib neeg uas tsis muaj keeb kwm ntawm tsis meej pem hauv lawv tsev neeg. Tsis tshua muaj, Russell - Silver Syndrome tuaj yeem khiav hauv tsev neeg. Autosomal tseem ceeb qub txeeg qub teg txhais tau tias ib daim qauv ntawm a caj kev hloov pauv hauv txhua lub cell yog txaus los ua rau tsis meej pem.

Ib tus kuj tseem yuav nug tau, Russell Silver syndrome tuaj yeem kho tau?

Kev kho mob rau Russell - Nyiaj Syndrome Kev kho mob kom pab nrog kev loj hlob thiab kev txhim kho suav nrog: cov sijhawm noj zaub mov zoo nrog cov khoom noj txom ncauj tshwj xeeb thiab sijhawm noj mov. kev loj hlob hormone txhaj tshuaj. luteinizing hormone-tso kev kho (cov tshuaj tso tawm hauv poj niam kom ua rau muaj qe menyuam txhua hli)

Lub neej expectancy ntawm ib tug neeg uas muaj Russell Silver syndrome yog dab tsi?

Txawm hais tias cov tub ntxhais hluas thiab cov neeg laus nrog Russell - Silver Syndrome yuav luv dua qhov nruab nrab, tus syndrome tsis cuam tshuam loj lub neej expectancy . Russell - Silver Syndrome tam sim no xav tias yog teeb meem caj ces, tshwm sim los ntawm kev txawv txav hauv chromosome 7 lossis chromosome 11.

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