![Puas yog Porphyria yog kab mob ntshav? Puas yog Porphyria yog kab mob ntshav?](https://i.answers-medical.com/preview/medical-health/14046574-is-porphyria-a-blood-disease-j.webp)
Video: Puas yog Porphyria yog kab mob ntshav?
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2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Porphyria (por-FEAR-e-uh) hais txog pab pawg ntawm cov teeb meem uas tshwm sim los ntawm kev tsim cov tshuaj lom neeg uas tsim cov tshuaj porphyrin hauv koj lub cev. Porphyrins Nws yog ib qho tseem ceeb rau kev ua haujlwm ntawm hemoglobin - cov protein hauv koj cov liab ntshav cov hlwb uas txuas rau porphyrin, khi hlau, thiab nqa oxygen rau koj lub cev thiab cov ntaub so ntswg.
Ib yam li ntawd, koj tuaj yeem nug, Porphyria puas yog ntshav tsis txaus?
Porphyrias yog ib pab pawg uas tsis tshua muaj txiaj ntsig ntshav tsis txaus . Cov neeg nrog cov no teeb meem Tsis txhob ua heme, ib feem ntawm hemoglobin (protein liab ntshav cov cell uas nqa oxygen) kom raug. Heme yog tsim los ntawm porphyrin (ib txwm muaj cov organic sib txuas hauv lub cev) khi rau hlau.
Ib sab saum toj no, Porphyria puas yog mob qog noj ntshav? Kev tshuaj xyuas cov ntaub ntawv qhia pom tias porphyria cutanea tarda (PCT), thiab tejzaum nws mob sib quas ntus porphyria kuj, yuav tshwm sim ntau dua li qhov xav tau ntawm cov neeg mob siab thawj mob qog noj ntshav , tshwj xeeb tshaj yog thaum muaj kab mob cirrhosis. Lymphomas thiab PCT kuj tseem muaj feem cuam tshuam, txawm tias qhov no tsis tshua muaj ntaub ntawv zoo.
Tsis tas li, puas yog porphyria yog kab mob autoimmune?
Mob sib quas ntus porphyria (AIP) yog qhov teeb meem kev zom zaub mov tsis tshua muaj tshwm sim los ntawm ib nrab ntawm cov enzyme hydroxymethylbilane synthase (tseem hu ua porphobilinogen deaminase). Qhov kev tsis txaus enzyme no tuaj yeem ua rau muaj cov porphyrin precursors hauv lub cev.
Dab tsi ua porphyria ua rau lub cev?
Porphyria (por-FEAR-e-uh) hais txog pab pawg ntawm cov teeb meem uas tshwm sim los ntawm kev sib sau ntawm cov tshuaj ntuj uas tsim cov tshuaj porphyrin hauv koj lub cev. lub cev . Porphyrins yog Qhov tseem ceeb rau kev ua haujlwm ntawm hemoglobin - ib qho protein hauv koj cov qe ntshav liab uas txuas rau porphyrin, khi hlau, thiab nqa oxygen rau koj lub cev thiab cov ntaub so ntswg.
Pom zoo:
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Kev kho tus kab mob vais lav sib txawv li cas nrog kev kho tus kab mob kab mob?
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Raws li koj tuaj yeem xav, kab mob kis tau los ntawm cov kab mob, thiab cov kab mob kis tau los ntawm cov kab mob. Tej zaum qhov sib txawv tseem ceeb tshaj plaws ntawm cov kab mob thiab cov kab mob yog tias cov tshuaj tua kab mob feem ntau tua cov kab mob, tab sis lawv tsis zoo rau cov kab mob
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Puas yog cov tshuaj tua kab mob tua kab mob tua kab?
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Ua kom nrawm hydrogen peroxide (uas yog Kev Cawm Seej yog ib lub npe) yog peb nyiam tshuaj tua kab mob. Thaum diluted kom tsim nyog, ua kom nrawm hydrogen peroxide ua txoj haujlwm zoo tshem tawm ib puag ncig uas muaj kab mob los ntawm tus kab mob kis, tab sis nws tsis tau raug tshuaj xyuas rau kev nyab xeeb lossis sau npe rau siv ua cov khoom siv tshuaj pleev