Puas muaj kev kho sai sai rau hemophilia?
Puas muaj kev kho sai sai rau hemophilia?

Video: Puas muaj kev kho sai sai rau hemophilia?

Video: Puas muaj kev kho sai sai rau hemophilia?
Video: nkauj tawm tshiab yuav tawm sai sai no 2024, Lub rau hli ntuj
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Muaj tam sim no tsis muaj kho rau hemophilia , tab sis cov neeg mob tuaj yeem kho nrog kev tso ntshav khov. “Cov tshuaj tiv thaiv no tuaj yeem ua rau cov protein tsis zoo uas nws yuav tsis kho lossis tiv thaiv lawv los ntshav. Qhov no tshwm sim txog li 30 feem pua lossis ntau dua ntawm cov neeg mob hnyav hemophilia A (qhov tseem ceeb VIII tsis txaus).

Ntxiv mus, puas tuaj yeem kho tus mob hemophilia lossis kho tau?

Lub sijhawm no tsis muaj kho rau hemophilia . Txawm li cas los xij, muaj kev cia siab zoo hauv kev kho mob hu ua kev kho noob neej. Nyob rau hauv tsawg tus neeg nrog hemophilia leej twg tau hloov daim siab, lawv hemophilia ua yog kho . Qhov no yog vim qhov sib txuam ua ke tau tsim hauv lub siab.

Qhov thib ob, cov kev kho mob yav tom ntej rau hemophilia yog dab tsi? Hauv yav tom ntej , ntau hom kev tshaj lij kev kho mob xws li noob neej kev kho mob , cell kev kho mob thiab cov ntaub so ntswg engineering, nrog rau kev tsim kho tshiab tam sim no ua rau pluripotent qia hlwb (iPSC) thev naus laus zis, tuaj yeem muab suav tsis txheeb rau kev siv tshuaj kho mob rau kev kho mob ntawm paub tseeb kab mob monogenic suav nrog hemophilia.

Hauv qhov no, tam sim no qhov xwm txheej ntawm kev tshawb fawb txog hemophilia puas muaj kev kho sai sai?

Muaj yog tam sim no tsis muaj kho rau hemophilia . Siv tau kev kho mob muaj nyob, tab sis lawv kim heev thiab koom nrog kev txhaj tshuaj tas mus li ob peb zaug hauv ib lub lis piam los tiv thaiv los ntshav.

Puas tuaj yeem tiv thaiv hemophilia?

Hemophilia yog caj ces (tau txais) kab mob thiab tsis tuaj yeem yog tiv thaiv . Kev sab laj txog caj ces, kev txheeb xyuas cov neeg nqa khoom los ntawm kev kuaj kab mob molecular, thiab kev kuaj mob ua ntej yug menyuam muaj los pab cov tib neeg nkag siab txog lawv txoj kev pheej hmoo ntawm kev muaj menyuam. hemophilia.

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