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Video: Dab tsi ua rau porphyria?
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2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Cov teeb meem no feem ntau tau txais, txhais tau tias lawv yog ua los ntawm qhov txawv txav ntawm cov noob tau dhau los ntawm niam txiv mus rau menyuam yaus. Thaum ib tug neeg muaj ib tug porphyria , hlwb tsis hloov lub cev tshuaj hu ua cov porphyrins thiab porphyrin ua ntej rau heme, cov khoom uas muab ntshav nws cov xim liab.
Txog qhov no, dab tsi tuaj yeem ua rau porphyria?
Porphyria tuaj yeem ua tau ua ua rau los ntawm cov tshuaj (barbiturates, ua kom tsaug zog, tshuaj tiv thaiv menyuam yaus, sedatives), tshuaj lom neeg, yoo mov, haus luam yeeb, haus dej cawv, kis kab mob, muaj kev nyuaj siab thiab lub cev muaj zog, cov tshuaj hormones coj khaub ncaws, thiab raug lub hnub. Tawm tsam ntawm porphyria tuaj yeem txhim kho ntau teev los yog hnub thiab kav rau hnub los yog lis piam.
Ib yam li ntawd, vim li cas porphyria hu ua tus kab mob vampire? Cov kab mob tau piav qhia thaum ntxov li 370 BC los ntawm Hippocrates. Lub hauv paus txheej txheem tau piav qhia thawj zaug los ntawm Felix Hoppe-Seyler xyoo 1871. Lub npe porphyria yog los ntawm Greek πορφύρα, porphyra, lub ntsiab lus "ntshav", hais txog xim ntawm cov zis uas tuaj yeem tshwm sim thaum tawm tsam.
Ua raws li qhov xav tau, porphyria cuam tshuam rau lub cev li cas?
Txhua yam ntawm porphyria koom nrog teeb meem hauv kev tsim cov heme. Heme yog ib feem ntawm hemoglobin, cov protein hauv cov qe ntshav liab uas nqa oxygen los ntawm koj lub ntsws mus rau txhua qhov ntawm koj lub cev. lub cev . Hauv daim tawv nqaij porphyria , cov cov porphyrins ua rau ntawm daim tawv nqaij, thiab thaum raug tshav ntuj, ua rau muaj tsos mob.
Puas yog porphyria ua rau vwm?
Keeb kwm thiab cov kws tshawb fawb tau tawm tsam ntev los txheeb xyuas qhov ua ntawm King George lub npe nrov " kev vwm . " Rov qab rau xyoo 1969, ib txoj kev tshawb fawb luam tawm hauv Scientific American pom tias nws muaj porphyria , ib qho ntshav tsis meej pem uas tuaj yeem ua rau ntxhov siab vim, nyob tsis tswm, insomnia, tsis meej pem, paranoia thiab ua rau pom kev.
Pom zoo:
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