Cov txheej txheem:

Dab tsi yog prions 11?
Dab tsi yog prions 11?

Video: Dab tsi yog prions 11?

Video: Dab tsi yog prions 11?
Video: prions 2024, Lub Xya hli ntuj
Anonim

Prions yog cov kab mob sib kis tau ua rau muaj ntau yam kab mob neurodegenerative hauv cov tsiaj, xws li, Creutzfeldt Jakob kab mob. Qhov no tshwm sim vim qhov txawv txav ntawm cov proteins hauv lub hlwb. Lawv tuaj yeem zom cov nucleic acids tab sis tau txais cov tshuaj uas tsis muaj cov protein.

Ntxiv mus, dab tsi yog cov piv txwv ntawm prions?

Hom kab mob prion muaj xws li:

  • CJD. Ib tug neeg tuaj yeem tau txais tus mob no, uas yog hu ua tsev neeg CJD.
  • Variant CJD.
  • Variably protease-sensitive prionopathy (VSPr).
  • Gerstmann-Sträussler-Scheinker kab mob (GSS).
  • Kuru.
  • Kev tuag insomnia (FI).

Dab tsi yog prions paub ua rau? Prion kab mob yog ua los ntawm cov ntaub ntawv tsis raug ntawm prion protein, ib paub uas PrP. Tib neeg forms of prion Cov kab mob feem ntau yog cov npe Creutzfeldt-Jakob kab mob (CJD), kev tuag hauv tsev neeg insomnia (FFI), Gertsmann-Straussler-Scheinker syndrome (GSS), kuru thiab variably protease-sensitive prionopathy (VPSPr).

Dhau li, dab tsi yog prion ib txwm?

Paub daws teeb. PrPc yog a li qub cell-surface glycoprotein uas yog conformationally characterized los ntawm ob alpha helices thiab ob complex-hom N-txuas oligosaccharide chains. Cov protein no yog qhov tshwj xeeb hauv nws qhov kev nyiam ua rau yuam kev mus rau hauv cov kab mob neurodegenerative ua rau muaj protein ntau sib kis kab mob, hu ua a prion.

Puas yog prion yog kab mob lossis kab mob?

' Prion ' yog ib lo lus thawj zaug siv los piav qhia txog tus kab mob sib kis tsis zoo uas lub luag haujlwm rau ntau yam kab mob neurodegenerative pom hauv cov tsiaj, suav nrog tus kab mob Creutzfeldt-Jakob (CJD) hauv tib neeg. (Tag nrho cov kab mob uas twb paub lawm, xws li kab mob thiab kab mob , muaj cov nucleic acids, uas ua rau lawv rov tsim dua.)

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