Video: Leukodystrophy yog dab tsi?
2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Leukodystrophies yog ib pab pawg uas tsis tshua muaj, vam meej, cov txheej txheem metabolic, kab mob hauv lub cev uas cuam tshuam rau lub hlwb, tus txha caj qaum thiab feem ntau yog cov hlab ntsha ib leeg. Txhua yam ntawm leukodystrophy yog tshwm sim los ntawm cov noob tshwj xeeb txawv txav uas ua rau kev txhim kho txawv txav lossis puas tsuaj ntawm cov xim dawb (myelin sheath) ntawm lub hlwb.
Kuj paub yog, koj tuaj yeem nyob ntev nrog leukodystrophy li cas?
Kev ua neej nyob feem ntau nyob ntawm lub hnub nyoog ntawm tus neeg yog xub kuaj mob. Tus kab mob no zuj zus sai dua thaum nws kuaj pom thaum muaj hnub nyoog ntxov. Cov menyuam yaus tau kuaj pom tias muaj cov me nyuam mos MLD lig nyob lwm tsib rau 10 xyoo. Hauv MLD cov hluas, lub neej cia siab yog 10 mus rau 20 xyoo tom qab kuaj mob.
Tom qab ntawd, lo lus nug yog, puas muaj kev kho rau leukodystrophy? Muaj yog tsis muaj kho rau ntau hom leukodystrophy . Kho nws nyob ntawm cov hom, thiab kws kho mob nyob cov cov tsos mob ntawm cov kab mob nrog tshuaj thiab yam tshwj xeeb ntawm lub cev, ua haujlwm, thiab hais lus kev kho mob.
Yog li ntawd, yog leukodystrophy tuag?
Lub sij hawm leukodystrophy yog siv rau ib pab pawg ntawm cov kab mob tsis tshua muaj caj ces uas cuam tshuam nrog lub hlwb thiab / lossis qaum qaum cov teeb meem dawb. Qee yam ntawm cov kab mob no pib thaum tseem me, loj hlob sai, thiab yog tuag taus , thaum lwm tus tsuas yog cuam tshuam rau cov neeg laus lossis kev vam meej qeeb dhau xyoo lawm.
Puas yog leukodystrophy yog kab mob autoimmune?
Leukodystrophies yog ib pab pawg uas feem ntau tau txais txiaj ntsig teeb meem yam ntxwv ntawm kev puas tsuaj ntawm cov teeb meem dawb hauv lub hlwb. Lwm yam demyelinating kab mob feem ntau tsis congenital thiab muaj tshuaj lom los yog autoimmune ua.
Pom zoo:
Dab tsi yog glycoprotein dab tsi yog ib qho ntawm kev siv glycoproteins?
Glycoproteins yog cov protein uas muaj cov oligosaccharide saw (glycans) covalently txuas nrog cov amino acid sab-saw. Glycoproteins kuj tseem yog ib qho tseem ceeb ua ke ntawm cov protein, uas lawv ua lub luag haujlwm hauv kev sib cuam tshuam ntawm tes -cell
Dab tsi yog cov khoom siv hauv lub cev zom zaub mov thiab lawv lub luag haujlwm yog dab tsi?
Cov khoom siv hauv lub cev zom zaub mov suav nrog cov hniav, tus nplaig, cov qog ua kua qaub, daim siab, lub zais zis, thiab txiav txiav. Txhawm rau ua tiav lub hom phiaj ntawm kev muab lub zog thiab khoom noj khoom haus rau lub cev, rau lub luag haujlwm tseem ceeb nyob hauv cov txheej txheem zom zaub mov: nqos. Kev zais
Dab tsi yog qhov kev nkag siab tsis tu ncua thiab dab tsi yog qhov loj me me qhov ntev xim tsis tu ncua zoo li qub)?
Kev nkag siab tsis tu ncua, tseem hu ua qhov tsis sib xws, lossis qhov tshwm sim tsis tu ncua, kev nyiam tsiaj thiab tib neeg kom pom cov khoom paub zoo li muaj tus qauv zoo, qhov loj me, xim, lossis qhov chaw tsis hais txog kev hloov pauv ntawm lub kaum sab xis ntawm kev xav, nrug deb, lossis teeb pom kev zoo
Lub cev tseem ceeb ntawm lub plab zom mov yog dab tsi thiab lawv lub luag haujlwm yog dab tsi?
Cov khoom siv hauv lub cev zom zaub mov suav nrog cov hniav, tus nplaig, cov qog ua kua qaub, daim siab, lub zais zis, thiab txiav txiav. Txhawm rau ua tiav lub hom phiaj ntawm kev muab lub zog thiab khoom noj khoom haus rau lub cev, rau lub luag haujlwm tseem ceeb nyob hauv cov txheej txheem zom zaub mov: nqos. Kev zais. Sib tov thiab txav mus los. Digestion. Kev nqus. Kev tshem tawm
Koj tuaj yeem nyob nrog leukodystrophy ntev npaum li cas?
Lifespan feem ntau nyob ntawm lub hnub nyoog uas tus neeg tau kuaj pom thawj zaug. Tus kab mob no zuj zus sai dua thaum nws kuaj pom thaum muaj hnub nyoog ntxov. Cov menyuam yaus uas tau kuaj pom tias muaj menyuam mos liab MLD feem ntau nyob lwm tsib mus rau 10 xyoo. Hauv MLD cov hluas, lub neej cia siab yog 10 txog 20 xyoo tom qab kuaj mob