![Vim li cas cystic fibrosis ua rau cov tawv nqaij qab ntsev? Vim li cas cystic fibrosis ua rau cov tawv nqaij qab ntsev?](https://i.answers-medical.com/preview/medical-health/14190031-why-does-cystic-fibrosis-cause-salty-skin-j.webp)
2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Raws li cov dej ntws tawm, cov cua sov raug tshem tawm, thiab lub cev txias. Hauv cov neeg uas muaj cystic fibrosis , ntsev mus rau lub cov tawv nqaij nto nrog dej thiab tsis reabsorbed. Vim li no, cov tawv nqaij ntawm tus me nyuam uas muaj cystic fibrosis yog txawv txav qab ntsev.
Ib yam li ntawd, nws tau nug, vim li cas kuv cov hws thiaj qab heev?
Piv txwv li, hws kuj muaj ammonia thiab urea, uas yog tsim los ntawm lub cev thaum nws zom cov proteins ntawm cov zaub mov koj noj. Hws kuj muaj qab zib thiab ntsev, xws li sodium, chloride, thiab potassium. Qhov no piav txog qhov qab ntsev saj koj tau ntsib thaum poob ntawm hws nrhiav nws txoj kev rau koj saj buds.
Ib yam li ntawd, vim li cas cystic fibrosis muaj ntau dua hauv Caucasian? Cystic fibrosis hauv Caucasian cov pejxeem. Cystic fibrosis yog ua tau ntau ntau dua hauv dawb Caucasian cov pejxeem. Cov kev sib txawv no tau piav qhia los ntawm qhov tseeb tias CF yog kab mob caj ces, vim muaj ob qho kev hloov pauv hauv CFTR gene (ib tus ntawm leej txiv thiab ib tus los ntawm leej niam).
Ua raws li qhov no hauv kev txiav txim siab, hom ntaub so ntswg twg feem ntau cuam tshuam los ntawm cov hnoos qeev ntau dhau ua rau cystic fibrosis?
Cystic fibrosis ( CF ) yog ib yam kab mob uas ua rau lub cev ua mucus uas yog tuab heev thiab nplaum. Cov hnoos qeev yog tuab dua li ib txwm vim CF cuam tshuam cov hlwb hauv epithelium (tshaj tawm: eh-puh-THEE-lee-um), txheej ntawm cov cell uas kab cov kab hauv kab hauv lub cev.
Puas yog cystic fibrosis ua rau tawm hws ntau dhau?
Cov tsos mob tseem ceeb ntawm CF yog cov hnoos qeev ua los ntawm cystic fibrosis transmembrane conductance regulator (CFTR). CFTR hloov txoj kev ntsev txav hauv lub cev, uas tseem cuam tshuam rau txoj kev uas lub cev tawm hws. Koj lub cev ua kom nws tus kheej txias los ntawm kev tso tawm hws . Txoj kev ceev tshaj plaws uas tsis muaj ntsev cuam tshuam rau lub cev yog lub cev qhuav dej.
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Kev tiv thaiv thiab kev tiv thaiv tej zaum yuav muaj xws li cov hauv qab no: Kev zam ntawm tus kab mob staphylococcal thawj zaug uas yuav ua rau muaj cov kab mob lom. Kev kho mob raws sijhawm ntawm cov kab mob staphylococcal tsim. Kev txheeb xyuas thiab kev kho tus kab mob asymptomatic
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Dermatitis yog lo lus dav dav uas piav txog kev ua rau tawv nqaij. Dermatitis yog ib yam mob uas muaj ntau yam ua rau thiab tshwm sim ntau yam. Nws feem ntau yog khaus, tawv nqaij qhuav los yog pob khaus ntawm daim tawv nqaij o, reddened
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txog 2 hli Ua raws li qhov no hauv kev txiav txim siab, tuab npaum li cas ntawm cov epidermis nyob tom qab? Dermis thiab subcutaneous rog Nws yog tuab (nruab nrab 1 txog 4 hli) tshaj li daim tawv nqaij uas yog hais txog nyias li daim ntawv.
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Hauv cystic fibrosis (CF), cov ducts hauv lub lauj kaub tais diav tau txhaws nrog cov tuab, nplaum nplaum. Cov hnoos qeev no thaiv cov enzymes los ntawm kev nkag mus rau cov zaub mov hauv cov hnyuv. Hmoov zoo, pancreatic enzyme hloov pauv lossis "enzymes" muaj los pab cov neeg nrog CF zom thiab nqus lawv cov zaub mov
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Lub epidermis yog tsim los ntawm stratified squamous epithelium. Lub dermis muaj cov ntaub so ntswg sib txuas, cov leeg nqaij du, thiab cov paj hlwb