Video: Yuav ua li cas fructose 1 phosphate inhibit Glycogenolysis?
2024 Tus sau: Michael Samuels | [email protected]. Kawg hloov kho: 2023-12-16 01:44
Fructose hmoov - 1 - phosphate depresses gluconeogenesis thiab txhawb glycolysis, thaum inorganic phosphate ploj lawm txwv ATP synthesis (Tshooj 14). Kev ntsuas glycogen yog inhibited los ntawm fructose qab zib - 1 - phosphate ntawm qib phosphorylase. Yog tias sucrose, fructose qab zib , thiab sorbitol raug tshem tawm los ntawm kev noj zaub mov, ua kom rov qab ua tiav.
Tsis tas li, vim li cas thiaj muaj fructose 1 phosphate txuam nrog?
Cov kev sib sau ntawm fructose 1 - phosphate ua rau glycogen synthesis hauv lub siab los ntawm kev ua kom muaj kev ua haujlwm enzymatic ntawm glycogen synthase b thaum muaj cov piam thaj 6- phosphate hauv vivo thiab los ntawm kev txhawb nqa kev ua kom muaj glycogen synthase.
Ib tus kuj yuav nug, vim li cas fructose intolerance ua rau hyperuricemia? Fructose hmoov -induced hyperuricemia : kev soj ntsuam hauv cov menyuam ib txwm muaj thiab hauv cov neeg mob uas muaj keeb kwm fructose intolerance thiab galactosemia. Hauv ob tus neeg mob nrog HFI, uric acid excretion tau nce plaub mus rau tsib npaug tom qab fructose qab zib kev tswj hwm; nce uric acid excretion nyob rau hauv HFI tshaj cov me nyuam ib txwm.
Tsis tas li kom paub yog, fructose intolerance ua rau hypoglycemia li cas?
Keeb kwm fructose intolerance yog ib qho kev ua txhaum hauv yug los ntawm cov metabolism nrog autosomal recessive qub txeeg qub teg. l-Sorbose tsis zoo los ntawm cov neeg mob no tab sis nws ua tsis induce hypoglycemia los yog hypophosphatemia. Hypoglycemia tom qab kev tswj hwm ntawm fructose qab zib los yog sorbitol yog vim muaj qhov thaiv ntawm cov piam thaj tso tawm.
Fructosemia yog dab tsi?
Hereditary fructosemia , kuj tseem muaj keeb tsis txaus ntseeg fructose, yog qhov tsis txaus ntseeg ntawm aldo-lase B (fructose biphosphate aldolase) hauv lub siab, raum, thiab hnyuv. 4. Kev hloov pauv tshwm sim hauv aldolase B noob, nyob ntawm chromosome 9q22.
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