Cov txheej txheem:

Koj puas tuaj yeem tsim kab mob kua txiv kua txiv hmab txiv ntoo?
Koj puas tuaj yeem tsim kab mob kua txiv kua txiv hmab txiv ntoo?

Video: Koj puas tuaj yeem tsim kab mob kua txiv kua txiv hmab txiv ntoo?

Video: Koj puas tuaj yeem tsim kab mob kua txiv kua txiv hmab txiv ntoo?
Video: Nas Ej Maiv Thoj Yuav Txiv Lawm Tiag Tiag 20/8/2021 2024, Tej zaum
Anonim

Puas yog tus neeg laus tuaj yeem ua tau txhim kho maple phoov cov kab mob zis ? Qee lub sij hawm tus kheej maple phoov tsw hauv zis los yog tawm hws tau tshwm sim hauv cov laus, cov menyuam noj qab nyob zoo lossis cov neeg laus uas tsis muaj tsos mob. Vim li cas rau qhov no tsis paub.

Ntxiv mus, ua li cas koj thiaj li tau txais maple phoov cov kab mob zis?

Maple phoov cov kab mob ( MSUD ) tau txais txiaj ntsig, uas txhais tau tias nws tau dhau los ntawm tsev neeg. Nws tshwm sim los ntawm qhov tsis xws luag ntawm 1 ntawm 3 noob. Cov neeg uas muaj tus mob no tsis tuaj yeem zom cov amino acids leucine, isoleucine, thiab valine. Qhov no ua rau kev tsim cov tshuaj no hauv cov ntshav.

Ib yam nkaus, cov kab mob maple phoov ntau npaum li cas? Maple phoov cov kab mob zis cuam tshuam txog kwv yees li ntawm 1 hauv 185, 000 menyuam mos thoob ntiaj teb. Qhov teeb meem tshwm sim ntau dua nyob hauv Old Order Mennonite cov pejxeem, nrog kwv yees li ntawm 1 hauv 380 menyuam mos.

Ib yam li ntawd, nws tau nug, cov tsos mob ntawm maple phoov cov kab mob li cas?

Qee cov tsos mob pib tus yam ntxwv ntawm MSUD qub yog:

  • ua tsis taus pa.
  • tsis qab los noj mov.
  • poob phaus.
  • tsis muaj peev xwm nqus tau.
  • chim siab.
  • qhov txawv ntawm maple qab zib tsw ntxhiab hauv pob ntseg, hws, thiab tso zis.
  • kev pw tsaug zog tsis xwm yeem.
  • hloov pauv ntu ntawm hypertonia (cov leeg nruj) thiab hypotonia (leeg nqaij limpness)

Hom kev hloov pauv dab tsi ua rau cov kab mob kua paug zis?

MSUD yog ua los ntawm kev hloov ( kev hloov pauv ) hauv peb hom sib txawv: BCKDHA, BCKDHB thiab DBT. Kev hloov pauv hauv cov noob no ua rau tsis tuaj lossis txo qis kev ua haujlwm ntawm tib neeg branched-chain alpha-ketoacid dehydrogenase complex (BCKAD) enzymes.

Pom zoo: